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What is the best way to detect infra-Hisian conduction abnormalities and prevent sudden cardiac death in myotonic dystrophy?
Myotonic dystrophy type 1 (DM1), also called Steinert's disease, is a multisystemic disorder for which the cardiologist is often consulted. Clinical manifestations of this disease, which involves multiple systems, may include muscle weakness, myotonia, multiple endocrinal disorders, cataract, respiratory insufficiency, conduction system disease, supraventricular arrhythmias, ventricular tachyarrhythmias and dilated cardiomyopathy.1–3 Sudden cardiac death is the second most common mode of death after respiratory failure in this population and occurs in up to one-third of patients.4 As DM1 becomes apparent in most cases by extracardiac manifestations, neurologists usually refer patients to...
Published By: MedWorm/DeathRecovery - Wednesday, 22 February
